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GAA / Alpha‑Glucosidase, Acid Antibody (aa761‑919) LS‑C294219
Alpha-Glucosidase, Acid antibody LS-C294219 is an unconjugated rabbit polyclonal antibody to human Alpha-Glucosidase, Acid (GAA). Validated for IHC and WB.
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Species:
Human, Monkey, Mouse, Rat, Bovine, Dog, Guinea pig, Hamster, Pig, Zebrafish
Applications:
Western blot
Species:
Human
Applications:
IHC, IHC - Paraffin, Western blot
Species:
Rat
Applications:
IHC, Western blot
Species:
Human, Mouse, Rat
Applications:
IHC, Western blot, Immunoprecipitation
Species:
Human, Mouse
Applications:
Western blot
Product Description
Alpha-Glucosidase, Acid antibody LS-C294219 is an unconjugated rabbit polyclonal antibody to human Alpha-Glucosidase, Acid (GAA). Validated for IHC and WB.
About GAA / Alpha-Glucosidase, Acid
GAA / Alpha-Glucosidase, Acid is acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene.
P10253
NM_000152
NP_000143.2
GAA Antibody, Acid maltase Antibody, Aglucosidase alfa Antibody, Glucosidase, alpha Antibody, Lysosomal alpha-glucosidase Antibody, Glucosidase, alpha acid Antibody, LYAG Antibody
Specifications
Target
Human GAA / Alpha-Glucosidase, Acid
Host
Rabbit
Reactivity
Human
(tested or 100% immunogen sequence identity)
Clonality
IgG
Polyclonal
Purification
Antigen-specific affinity chromatography followed by Protein A affinity chromatography
Modifications
Unmodified
Applications
- IHC
- Western blot (1:100 - 1:400)
- (applications tested for the base form of this product only)
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Performing IHC? See our complete line of Immunohistochemistry Reagents including antigen retrieval solutions, blocking agents
ABC Detection Kits and polymers, biotinylated secondary antibodies, substrates and more.
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Immunogen
Recombinant GaA (Ala761-Asn919) expressed in E. coli.
Epitope
aa761-919
Specificity
The antibody is a rabbit polyclonal antibody raised against GaA. It has been selected for its ability to recognize GaA in immunohistochemical staining and western blotting.
Usage
ELISA 1:100-1:5000; ICC 1:50-500; WB 1:50-400;
Presentation
PBS, pH 7.4, 0.02% sodium azide, 50% glycerol.
Storage
Avoid repeated freeze/thaw cycles. Store at 4°C for frequent use. Aliquot and store at -20°C for 12 months.
Restrictions
For research use only.
Guarantee
This antibody carries the LSBio 100% Guarantee.
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Customer Reviews (0)
Images
Western blot
Western blot of recombinant GAA. This image was taken for the unconjugated form of this product. Other forms have not been tested.
Western blot
Western blot of recombinant GAA. This image was taken for the unconjugated form of this product. Other forms have not been tested.
Western blot
Western blot of recombinant GAA. This image was taken for the unconjugated form of this product. Other forms have not been tested.
Western blot
Western blot of recombinant GAA. This image was taken for the unconjugated form of this product. Other forms have not been tested.
Requested From:
Date Requested: 7/19/2018
Date Requested: 7/19/2018
