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Anti-GAA / Alpha-Glucosidase, Acid Antibody (aa761-919) LS-C294219
Most Popular GAA / Alpha-Glucosidase, Acid Antibodies
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Details
| Human GAA / Alpha-Glucosidase, Acid | |
| Rabbit | |
| Human (tested or 100% immunogen sequence identity) | |
| IgG Polyclonal | |
| Unconjugated. Also available conjugated with Biotin, FITC. | |
| Antigen-specific affinity chromatography followed by Protein A affinity chromatography | |
| Unmodified |
Applications
- Western blot (1:100 - 1:400)
- (applications tested for the base form of this product only)
Specificity and Use
| Recombinant GaA (Ala761-Asn919) expressed in E. coli. | |
| aa761-919 | |
| The antibody is a rabbit polyclonal antibody raised against GaA. It has been selected for its ability to recognize GaA in immunohistochemical staining and western blotting. | |
| ELISA 1:100-1:5000; ICC 1:50-500; WB 1:50-400; |
Packaging
| PBS, pH 7.4, 0.02% sodium azide, 50% glycerol. | |
| Store at 4°C for frequent use. Aliquot and store at -20°C for up to 1 year. Avoid freeze/thaw cycles | |
| For research use only. |
About GAA / Alpha-Glucosidase, Acid
P10253
NM_000152
NP_000143.2
GAA Antibody, Acid maltase Antibody, Aglucosidase alfa Antibody, Glucosidase, alpha Antibody, Lysosomal alpha-glucosidase Antibody, Glucosidase, alpha acid Antibody, LYAG Antibody
GAA / Alpha-Glucosidase, Acid is acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene.
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Requested From:
Date Requested: 4/22/2018
Date Requested: 4/22/2018
