BCKDHA / BCKDE1A

branched chain keto acid dehydrogenase E1, alpha polypeptide

The branched-chain alpha-keto acid (BCAA) dehydrogenase (BCKD) complex is an innter mitochondrial enzyme complex that catalyzes the second major step in the catabolism of the branched-chain amino acids leucine, isoleucine, and valine. The BCKD complex consists of three catalytic components: a heterotetrameric (alpha2-beta2) branched-chain alpha-keto acid decarboxylase (E1), a dihydrolipoyl transacylase (E2), and a dihydrolipoamide dehydrogenase (E3). This gene encodes the alpha subunit of the decarboxylase (E1) component. Mutations in this gene result in maple syrup urine disease, type IA. Multiple transcript variants encoding different isoforms have been found for this gene.

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Products

Proteins (5)

Type

Over-Expression Lysate (2)

Recombinant (3)

Target

BCKDHA / BCKDE1A (5)

Publications

No (5)

Tag

GST (1)

GST, N-terminus (1)

His (1)

Myc-DDK (Flag) (2)

Species

Human (4)

Source

293T Cells (1)

E. coli (1)

HEK 293 Cells (1)

Wheat Germ Extract (2)

Purification

Purified (2)

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BCKDHA / BCKDE1A Protein (Over-Expression Lysate Myc-DDK (Flag)) (Full Length) - LS-G128669

Source:

HEK 293 Cells

Tag:

Myc-DDK (Flag)

Molecular Weight:

50.4 kDa

Price:

100 µg/$494

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Human BCKDHA / BCKDE1A Protein (Recombinant GST) (Full Length) - LS-G27605

Source:

Wheat Germ Extract

Tag:

GST

Molecular Weight:

74.69 kDa

Price:

10 µg/$479; 25 µg/$670

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Human BCKDHA / BCKDE1A Protein (Over-Expression Lysate Myc-DDK (Flag)) (Full Length) - LS-G74011

Source:

293T Cells

Tag:

Myc-DDK (Flag)

Molecular Weight:

50.4 kDa

Price:

20 µg/$150

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Human BCKDHA / BCKDE1A Protein (Recombinant GST, N-terminus) (aa347-445) - LS-G57879

Source:

Wheat Germ Extract

Tag:

GST, N-terminus

Price:

10 µg/$479; 25 µg/$670

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Human BCKDHA / BCKDE1A Protein (Recombinant His) - LS-G1166

Source:

E. coli

Tag:

His

Price:

10 µg/$311; 50 µg/$498; 20 µg/$386; 100 µg/$790; 250 µg/$1,278; 500 µg/$1,917

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